Orbital myositis and hypophysitis as manifestations of IgG4-related disease

Authors

  • Antonio Meseguer-Hernández Servicio de Cardiología, Hospital Universitario Santa Lucía, Cartagena, Murcia, España https://orcid.org/0009-0008-1924-6832
  • Tomás Bruno-Pérez Servicio de Medicina Interna, Hospital Universitario Santa Lucía, Cartagena, Murcia, España
  • Beatriz María Ferrín-López Servicio de Servicio de Pediatría, Hospital Universitario Virgen de la Arrixaca, Murcia, España
  • Francisco Buendía-Santiago Servicio de Cardiología, Hospital Universitario Santa Lucía, Cartagena, Murcia, España
  • María del Carmen Guirao-Balsalobre Servicio de Cardiología, Hospital Universitario Santa Lucía, Cartagena, Murcia, España https://orcid.org/0009-0001-4781-5173

DOI:

https://doi.org/10.32818/reccmi.a8n3a10

Keywords:

immunoglobulin G4-related disease, hypophysitis, myositis, eye

Abstract

IgG4 hypophysitis is a pathology found in non-functioning pituitary masses. We present the case of a 52-year-old woman with a history of orbital myositis of unclear etiology who came to our center for headache with alarm criteria and clinical signs of diabetes insipidus. The imaging study showed a pituitary mass causing panhypopituitarism. Analytically it highlights elevated serum levels of IgG4, so with the suspicion of the disease treatment is initiated with corticosteroids, with a great clinical improvement.

Downloads

Download data is not yet available.

Metrics

Metrics Loading ...

References

Ardila-Suarez O, Abril A, Gómez-Puerta JA. IgG4-related disease: a concise review of the current literature. Reumatol Clin. 2017; 13(3): 160-166. Accesible en: https://www.reumatologiaclinica.org/es-pdf-S1699258X16300535 (último acceso nov. 2023). DOI: https://doi.org/10.1016/j.reumae.2016.05.006

Sosa GA. Hipofisitis linfoplasmocitaria con expresión de IgG4. Rev Argent Endocrinol Metab 2017; 54: 76-82. Accesible en: https://www.sciencedirect.com/science/article/pii/S0326461016300808 (último acceso nov. 2023). DOI: https://doi.org/10.1016/j.raem.2017.01.001

Leporati P, Landek-Salgado MA, Lupi I, Chiovato L, Caturegli P. IgG4-related hypophysitis: a new addition to the hypophysitis spectrum. J Clin Endocrinol Metab. 2011; 96: 1971-1980. doi: https://doi.org/10.1210/jc.2010-2970 (último acceso nov. 2023). DOI: https://doi.org/10.1210/jc.2010-2970

McNab AA, McKelvie P. IgG4-related ophthalmic disease. Part II: clinical aspects. Ophthalmic Plast Reconstr Surg. 2015; 31(3): 167-78. doi: https://doi.org/10.1097/IOP.0000000000000364 (último acceso nov. 2023). DOI: https://doi.org/10.1097/IOP.0000000000000364

Wallace ZS, Naden RP, Chari S, et al. The 2019 American College of Rheumatology/European League Against Rheumatism classification criteria for IgG4-related disease. Ann Rheum Dis. 2020; 79(1): 77–87. Accesible en: https://acrjournals.onlinelibrary.wiley.com/doi/epdf/10.1002/art.41120 (último acceso nov. 2023).

Katz G, Stone JH. Clinical perspectives on IgG4-related disease and its classification. Annu Rev Med. 2022; 73: 545-562. Accesible en: https://www.annualreviews.org/doi/pdf/10.1146/annurev-med-050219-034449 (último acceso nov. 2023). DOI: https://doi.org/10.1146/annurev-med-050219-034449

Published

2023-12-31

How to Cite

1.
Meseguer-Hernández A, Bruno-Pérez T, Ferrín-López BM, Buendía-Santiago F, Guirao-Balsalobre M del C. Orbital myositis and hypophysitis as manifestations of IgG4-related disease. Rev Esp Casos Clin Med Intern [Internet]. 2023 Dec. 31 [cited 2024 Jul. 3];8(3):139-41. Available from: https://www.reccmi.com/RECCMI/article/view/915

Most read articles by the same author(s)