Syndrome Revealing Gastric MALT Lymphoma

Authors

  • Laurine Prinet Servicio de Medicina Interna, Hospital Universitario Virgen de las Nieves, Granada, España
  • Joaquín Escobar Sevilla Servicio de Medicina Interna, Hospital Universitario Virgen de las Nieves, Granada, España https://orcid.org/0000-0002-9210-2439
  • Sara Domingo Roa Servicio de Medicina Interna, Hospital Universitario Virgen de las Nieves, Granada, España
  • Ruben Lobato Cano Servicio de Medicina Interna, Hospital Universitario Virgen de las Nieves, Granada, España
  • Juan Diego Mediavilla García Servicio de Medicina Interna, Hospital Universitario Virgen de las Nieves, Granada, España

DOI:

https://doi.org/10.32818/reccmi.a6n2a5

Keywords:

RS3PE syndrome, paraneoplastic syndrome, Non-Hodking lymphoma, MALT.

Abstract

Remitting seronegative symmetric synovitis with pitting edema (RS3PE) syndrome is characterized by symmetric synovitis that affects the small joints of the hands and feet with pitting edema in these areas. The importance of identifying this entity lies in its association with underlying pathologies, mostly solid organ neoplasms (especially adenocarcinomas) and hematological ones. We present the case of a patient with recurrent seronegative symmetric synovitis with edema secondary to extranodal B-cell non-Hodking lymphoma associated with gastric lymphoid tissue (gastric MALT lymphoma).

Downloads

Download data is not yet available.

Metrics

Metrics Loading ...

References

McCarty D, O'duffy J, Pearson L, Hunter JB. Remitting Seronegative Symmetrical Synovitis With Pitting Edema: RS3PE Syndrome. JAMA: JAMA. 1985; 254(19): 2763-7. doi: https://doi.org/10.1001/jama.1985.03360190069027.

Finnell JA, Cuesta IA. Remitting seronegative symmetrical synovitis with pitting edema (RS3PE) syndrome: a review of the literature and a report of three cases. J Foot Ankle Surg. 2000; 39(3): 189-93. doi: https://doi.org/10.1016/s1067-2516(00)80021-6.

Russell EB, Hunter JB, Pearson L, McCarty DJ. Remitting, seronegative, symmetrical synovitis with pitting edema--13 additional cases. J Rheumatol. 1990; 17(5): 633-9.

Laidler NK, Delaney T. Remitting seronegative symmetric synovitis with pitting edema (RS3PE) with painful erythematous nodules. BMJ Case Rep. 2020; 13(4): e234197. doi: https://doi.org/10.1136/bcr-2019-234197.

Ciro Manzo. The Paraneoplastic Meaning of R3SPE (Remitting Seronegative Simmetrical Synovitis with Pitting Edema) Syndrome. J Med Oncl Ther 2016; 1 (2): 72-75. doi https://doi.org/10.35841/medical-oncology.1.2.72-75.

Cantini F, Salvarani C, Olivieri I. Paraneoplastic remitting seronegative symmetrical synovitis with pitting edema. Clin Exp Rheumatol. 1999; 17(6): 741-4.

Hegazi MO, Saleh F, Al Rashidi A, Yaktien MM. Synovitis with pitting edema as the presenting manifestation of systemic lupus erythematosus. Lupus. 2014; 23(10): 1069-72. doi: https://doi.org/10.1177/0961203314533601.

Arima K, Origuchi T, Tamai M, Iwanaga N, Izumi Y, Huang M et al. RS3PE syndrome presenting as vascular endothelial growth factor associated disorder. Ann Rheum Dis. 2005; 64(11): 1653-5. doi: https://doi.org/10.1136/ard.2004.032995.

Published

2021-08-31

How to Cite

1.
Prinet L, Escobar Sevilla J, Domingo Roa S, Lobato Cano R, Mediavilla García JD. Syndrome Revealing Gastric MALT Lymphoma. Rev Esp Casos Clin Med Intern [Internet]. 2021 Aug. 31 [cited 2024 Jul. 3];6(2):12-4. Available from: https://www.reccmi.com/RECCMI/article/view/650

Similar Articles

You may also start an advanced similarity search for this article.