Hipoacusia neurosensorial, ataxia cerebelosa y piramidalismo: una tríada sugerente de siderosis superficial del sistema nervioso central

Jaime Díaz-Real; Julia Fernández-Soto; Mariano Aguayo-Canela

doi:10.32818/reccmi.a4n3a14

Authors

Jaime Díaz-Real Servicio de Medicina Interna, Hospital Universitario Juan Ramón Jiménez, Huelva, Spain
Julia Fernández-Soto Servicio de Medicina Interna, Hospital Universitario Juan Ramón Jiménez, Huelva, Spain
Mariano Aguayo-Canela Servicio de Medicina Interna, Hospital Universitario Juan Ramón Jiménez, Huelva, Spain

DOI:

https://doi.org/10.32818/reccmi.a4n3a14

Keywords:

superficial siderosis, ataxia, hearing loss, cerebral amyloid angiopathy, brain magnetic resonance

Abstract

Superficial siderosis of the central nervous system is an underdiagnosed pathology. It is most likely produced because of persistent bleeding that causes hemosiderin deposition in the nervous structures. This generates oxidative damage in the glial tissue, which causes progressive central nervous system dysfunction. Symptoms depend on the affected areas. The diagnosis and characterization of superficial siderosis are mainly carried out by brain and spinal cord magnetic resonance imaging. In most cases its approach is surgical, although without providing significant benefit. Nowadays, no efficient treatment is available to stop the evolution of the disease.

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