Extensive myocarditis in a granulomatosis with polyan- geitis (Wegener)
DOI:
https://doi.org/10.32818/reccmi.a4n3a8Keywords:
antineutrophil cytoplasmic antibodies, systemic vasculitis, myocarditisAbstract
A 32 years-old woman, history of chronic rhinitis, rhinosinusal polyposis and eutocic delivery three weeks before, admitted to Cardiology for heart failure with elevated troponins and NT-proBNP. Bilateral and symmetric pulmonary nodules were detected in a thoracic CT scan. Echocardiography and cardiac magnetic resonance confirmed the presence of myocarditis. A biopsy of rhinosinusal polyps is compatible with granulomatosis with polyangiitis. In addition, mild renal involvement is detected due to the presence of microscopic hematuria and leukocyturia. She required treatment with corticosteroids and cyclophosphamide, after which her ventricular dysfunction symptoms improved.
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Copyright (c) 2019 María Cristina de Ybarra-Falcón, Gonzalo Cabezón-Villalba, Mario García-Gómez, Javier López-Díaz, José Alberto San Román-Calvar
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