Macrophage activation syndrome in relation to Still's disease. A potentially deadly combination
DOI:
https://doi.org/10.32818/reccmi.a10n1a2Keywords:
Still's disease, macrophage activation syndrome, hyperferritinemiaAbstract
Still's disease is a rare and potentially serious systemic inflammatory condition associated with macrophage activation syndrome. Diagnosis is by exclusion, requiring a high clinical-analytical suspicion and a negative screening for other probable causes (mainly infectious, malignant or autoimmune). In this context, it is especially difficult to obtain an accurate diagnosis in order to initiate optimal and early treatment. We describe a case of adult-onset Still's disease, with a probable incipient macrophage activation syndrome.
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Copyright (c) 2025 Marc Colomé Ayats, Paula Camila Álvarez-Schlegel, Carlota Mir-Castro, Aleix Bonet-Benavente, Javier Ramos-L´ázaro
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