Extranodal Rosai-Dorfman: a rare disease with a common clinical manifestation.
DOI:
https://doi.org/10.32818/reccmi.a5n2a6Keywords:
Rosai-Dorfman disease, bone, central nervous system, sinus histiocytosis, non-Langerhans cell histiocytosis.Abstract
Sinusoidal histiocytosis with massive lymphadenopathy or Rosai-Dorfman disease (RDD) is a benign proliferative disorder of histiocytes. It is most frequently seen in children and young adults but can occur at any age. The disease is more common in men and individuals of African descent. It is an uncommon entity with a variety of clinical manifestations. We present a case of extranodal RDD of complex diagnosis with bone involvement and the central nervous system. In this case, the biopsy was conclusive highlighting the distinctive aspects of this pathology
Downloads
Metrics
References
- Abla O, Jacobsen E, Picarsic J, Krenova Z, Jaffe R, Emile JF et al. Consensus recommendations for the diagnosis and clinical management of Rosai-Dorfman-Destombes disease. Blood. 2018; 131(26): 2877-2890. doi: https://doi.org/10.1182/blood-2018-03-839753.
- Goyal G, Ravindran A, Young JR, Shah MV, Bennani NN, Patnaik MM et al. Clinicopathological features, treatment approaches, and outcomes in Rosai-Dorfman disease. Haematologica. 2020 Jan 31;105(2):348-357. doi: https://doi.org/10.3324/haematol.2019.219626.
- Namoglu EC, Hughes ME, Plastaras JP, Landsburg DJ, Maity A, Nasta SD. Management and outcomes of sinus histiocytosis with massive lymphadenopathy (Rosai Dorfman Disease). Leuk Lymphoma. 2019: 1-7. doi: https://doi.org/10.1080/10428194.2019.1703971.
- Piris MA, Aguirregoicoa E, Montes-Moreno S, Celeiro-Muñoz C. Castleman Disease and Rosai-Dorfman Disease. Semin Diagn Pathol. 2018; 35(1): 44-53. doi: https://doi.org/10.1053/j.semdp.2017.11.014.
- Luo Z, Zhang Y, Zhao P, Lu H, Yang K, Zhang Y et al. Characteristics of Rosai-Dorfman Disease Primarily Involved in the Central Nervous System: 3 Case Reports and Review of Literature. World Neurosurg. 2017; 97: 58-63. doi: https://doi.org/10.1016/j.wneu.2016.09.084.
- Triana-Pérez AB, Sánchez-Medina Y, Pérez-Del Rosario PA, Millán-Corada AM, Gómez-Perals LF, Domínguez-Báez JJ. Enfermedad de Rosai-Dorfman intracraneal. Presentación de un caso y revisión de la literatura Neurocirugia (Astur). 2011; 22(3): 255-60. doi: https://doi.org/10.1016/S1130-1473(11)70021-5
- Mavrogenis AF, Igoumenou VG, Antoniadou T, Megaloikonomos PD, Agrogiannis G, Foukas P et al. Rare diseases of bone: Erdheim-Chester and Rosai-Dorfman non-Langerhans cell histiocytoses. EFORT Open Rev. 2018; 3(6): 381-390. doi: https://doi.org/10.1302/2058-5241.3.170047.
- Shah V, Mohyeldin A, London NR, Fritz J, Prevedello DM, Carrau RL et al. When a Meningioma Isn't: Endoscopic Endonasal Orbital Decompression and Biopsy of Skull Base Rosai-Dorfman Disease Treated Previously with Empiric Radiation Therapy. World Neurosurg. 2019 Dec 13;135:141-145. doi: https://doi.org/10.1016/j.wneu.2019.12.032.
Downloads
Published
How to Cite
Issue
Section
License
Copyright (c) 2020 María Carolina Fragozo-Ramos, Paola Andrea Ortiz-Marin, Marbel Karina Corzo-Pacheco, Cesar Redondo-Bermudez
This work is licensed under a Creative Commons Attribution-NonCommercial-NoDerivatives 4.0 International License.
Permite compartir, copiar y redistribuir el material en cualquier medio o formato, bajo los siguientes términos:
Reconocimiento: debe otorgar el crédito correspondiente, proporcionar un enlace a la licencia e indicar si se realizaron cambios. Puede hacerlo de cualquier manera razonable, pero no de ninguna manera que sugiera que el licenciante lo respalda a usted o su uso.
No comercial: no puede utilizar el material con fines comerciales.
No Derivados: si remezcla, transforma o construye sobre el material, no puede distribuir el material modificado.
Sin restricciones adicionales: no puede aplicar términos legales o medidas tecnológicas que restrinjan legalmente a otros de hacer cualquier cosa que permita la licencia.
