Sensorineural hearing loss, cerebellar ataxia and pyramidalism: a suggestive triad of superficial side- rosis of the central nervous system
DOI:
https://doi.org/10.32818/reccmi.a4n3a14Keywords:
superficial siderosis, ataxia, hearing loss, cerebral amyloid angiopathy, brain magnetic resonanceAbstract
Superficial siderosis of the central nervous system is an underdiagnosed pathology. It is most likely produced because of persistent bleeding that causes hemosiderin deposition in the nervous structures. This generates oxidative damage in the glial tissue, which causes progressive central nervous system dysfunction. Symptoms depend on the affected areas. The diagnosis and characterization of superficial siderosis are mainly carried out by brain and spinal cord magnetic resonance imaging. In most cases its approach is surgical, although without providing significant benefit. Nowadays, no efficient treatment is available to stop the evolution of the disease.
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Copyright (c) 2019 Jaime Díaz-Real, Julia Fernández-Soto, Mariano Aguayo-Canela
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